| 存储条件 |
|---|
| Product Name | HADH |
|---|---|
| Antibody Type | Primary Antibodies |
| Antigen Alias | 3 ketoacyl Coenzyme A (CoA) thiolase alpha subunit antibody 3 oxoacyl CoA thiolase antibody 78 kDa gastrin binding protein antibody 78 kDa gastrin-binding protein antibody ECHA antibody ECHA_HUMAN antibody GBP antibody HADH antibody HADHA antibody Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit antibody LCEH antibody LCHAD antibody Long chain 3-hydroxyacyl-CoA dehydrogenase antibody Mitochondrial long chain 2 enoyl Coenzyme A (CoA) hydratase alpha subunit antibody Mitochondrial long chain L 3 hydroxyacyl Coenzyme A dehydrogenase alpha subunit antibody Mitochondrial trifunctional enzyme alpha subunit antibody Mitochondrial trifunctional protein alpha subunit antibody MTPA antibody Thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit antibody TP ALPHA antibody TP-alpha antibody Trifunctional enzyme subunit alpha mitochondrial precursor antibody |
| Product description | Hydroxyacyl-Coenzyme A dehydrogenase also known as HADH is an enzyme which in humans is encoded by the HADH gene. This gene is a member of the 3-hydroxyacyl-CoA dehydrogenase gene family. The encoded protein functions in the mitochondrial matrix to catalyze the oxidation of straight-chain 3-hydroxyacyl-CoAs as part of the beta-oxidation pathway. Its enzymatic activity is highest with medium-chain-length fatty acids. Mutations in this gene cause one form of familial hyperinsulinemic hypoglycemia. A deficiency is associated with 3-hydroxyacyl-coenzyme A dehydrogenase deficiency. |
| Immunogen | peptide |
| Clonality | Polyclonal |
|---|---|
| Isotype | IgG |
| Host Species | Rabbit |
| Tested Applications | WBICCIHC |
| WB:1:500 ICC:1:50-1:100 | |
| Species Reactivity | HumanMouseRat |
| Concentration | 1mg/ml |
| Alternative Names | 3 ketoacyl Coenzyme A (CoA) thiolase alpha subunit antibody 3 oxoacyl CoA thiolase antibody 78 kDa gastrin binding protein antibody 78 kDa gastrin-binding protein antibody ECHA antibody ECHA_HUMAN antibody GBP antibody HADH antibody HADHA antibody Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit antibody LCEH antibody LCHAD antibody Long chain 3-hydroxyacyl-CoA dehydrogenase antibody Mitochondrial long chain 2 enoyl Coenzyme A (CoA) hydratase alpha subunit antibody Mitochondrial long chain L 3 hydroxyacyl Coenzyme A dehydrogenase alpha subunit antibody Mitochondrial trifunctional enzyme alpha subunit antibody Mitochondrial trifunctional protein alpha subunit antibody MTPA antibody Thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit antibody TP ALPHA antibody TP-alpha antibody Trifunctional enzyme subunit alpha mitochondrial precursor antibody |
|---|---|
| Molecular Weight(MW) | 34 kDa |
| Cellular Localization | Mitochondrial matrix |
| SwissProt ID | Q16836 |
|---|

Application
Fig1: Western blot analysis on cell lysates using anti- HADH rabbit polyclonal antibodies.| Positive Control | MCF-7, human kidney |
|---|---|
| Application Notes | WB:1:500 ICC:1:50-1:100 |
| Form | Liquid |
|---|---|
| Storage Instructions | Store at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles. |
| Storage Buffer | 1*TBS (pH7.4), 0.5%BSA, 40%Glycerol. Preservative: 0.05% Sodium Azide. |
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