HADH

HADH

产品编号 :
英文名称 :
中文名称 :
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包装规格 交货周期 质量标准 目录价 会员专享价 数量
20ul 现货2-3天 原装正品
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50ul 现货2-3天 原装正品
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100ul 现货2-3天 原装正品
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基础信息
存储条件
产品详情
Product Profile
Product NameHADH
Antibody TypePrimary Antibodies
Antigen Alias3 ketoacyl Coenzyme A (CoA) thiolase alpha subunit antibody 3 oxoacyl CoA thiolase antibody 78 kDa gastrin binding protein antibody 78 kDa gastrin-binding protein antibody ECHA antibody ECHA_HUMAN antibody GBP antibody HADH antibody HADHA antibody Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit antibody LCEH antibody LCHAD antibody Long chain 3-hydroxyacyl-CoA dehydrogenase antibody Mitochondrial long chain 2 enoyl Coenzyme A (CoA) hydratase alpha subunit antibody Mitochondrial long chain L 3 hydroxyacyl Coenzyme A dehydrogenase alpha subunit antibody Mitochondrial trifunctional enzyme alpha subunit antibody Mitochondrial trifunctional protein alpha subunit antibody MTPA antibody Thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit antibody TP ALPHA antibody TP-alpha antibody Trifunctional enzyme subunit alpha mitochondrial precursor antibody
Product descriptionHydroxyacyl-Coenzyme A dehydrogenase also known as HADH is an enzyme which in humans is encoded by the HADH gene. This gene is a member of the 3-hydroxyacyl-CoA dehydrogenase gene family. The encoded protein functions in the mitochondrial matrix to catalyze the oxidation of straight-chain 3-hydroxyacyl-CoAs as part of the beta-oxidation pathway. Its enzymatic activity is highest with medium-chain-length fatty acids. Mutations in this gene cause one form of familial hyperinsulinemic hypoglycemia. A deficiency is associated with 3-hydroxyacyl-coenzyme A dehydrogenase deficiency.
Immunogenpeptide
Key Feature
ClonalityPolyclonal
IsotypeIgG
Host SpeciesRabbit
Tested ApplicationsWBICCIHC

WB:1:500
ICC:1:50-1:100
Species ReactivityHumanMouseRat
Concentration1mg/ml
Target Information
Alternative Names3 ketoacyl Coenzyme A (CoA) thiolase alpha subunit antibody 3 oxoacyl CoA thiolase antibody 78 kDa gastrin binding protein antibody 78 kDa gastrin-binding protein antibody ECHA antibody ECHA_HUMAN antibody GBP antibody HADH antibody HADHA antibody Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit antibody LCEH antibody LCHAD antibody Long chain 3-hydroxyacyl-CoA dehydrogenase antibody Mitochondrial long chain 2 enoyl Coenzyme A (CoA) hydratase alpha subunit antibody Mitochondrial long chain L 3 hydroxyacyl Coenzyme A dehydrogenase alpha subunit antibody Mitochondrial trifunctional enzyme alpha subunit antibody Mitochondrial trifunctional protein alpha subunit antibody MTPA antibody Thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit antibody TP ALPHA antibody TP-alpha antibody Trifunctional enzyme subunit alpha mitochondrial precursor antibody
Molecular Weight(MW)34 kDa
Cellular LocalizationMitochondrial matrix
Database Links
SwissProt IDQ16836
Application

Application

Fig1: Western blot analysis on cell lysates using anti- HADH rabbit polyclonal antibodies.
Positive ControlMCF-7, human kidney
Application NotesWB:1:500
ICC:1:50-1:100
Additional Information
FormLiquid
Storage InstructionsStore at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles.
Storage Buffer1*TBS (pH7.4), 0.5%BSA, 40%Glycerol. Preservative: 0.05% Sodium Azide.


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