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alpha 1-antitrypsin

alpha 1-antitrypsin

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包装规格 交货周期 质量标准 目录价 会员专享价 数量
20ul 现货2-3天 原装正品
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50ul 现货2-3天 原装正品
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100ul 现货2-3天 原装正品
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基础信息
存储条件
产品详情
Product Profile
Product Namealpha 1-antitrypsin
Antibody TypePrimary Antibodies
Antigen AliasA1A antibody A1AT antibody A1AT_HUMAN antibody AAT antibody Alpha 1 antiproteinase antibody Alpha 1 antitrypsin antibody Alpha 1 antitrypsin null antibody Alpha 1 protease inhibitor antibody Alpha-1 protease inhibitor antibody Alpha-1-antiproteinase antibody alpha1 proteinase inhibitor antibody Alpha1AT antibody Dom1 antibody PI antibody PI1 antibody PRO2275 antibody Serine (or cysteine) proteinase inhibitor clade A member 1 antibody Serine protease inhibitor 1-1 antibody Serine protease inhibitor A1a antibody Serpin A1 antibody Serpin A1a antibody Serpin peptidase inhibitor clade A member 1 antibody Serpina1 antibody Short peptide from AAT antibody SPAAT antibody Spi1-1 antibody
Product descriptionAlpha 1-Antitrypsin is a inhibitor of serine proteases. Its primary target is elastase, but it also has a moderate affinity for plasmin and thrombin. It Irreversibly inhibits trypsin, chymotrypsin and plasminogen activator. The aberrant form inhibits insulin-induced NO synthesis in platelets, decreases coagulation time and has proteolytic activity against insulin and plasmin. Defects in SERPINA1 are the cause of alpha-1-antitrypsin deficiency (A1ATD). A disorder whose most common manifestation is emphysema, which becomes evident by the third to fourth decade. A less common manifestation of the deficiency is liver disease, which occurs in children and adults, and may result in cirrhosis and liver failure.
Immunogenpeptide
Key Feature
ClonalityPolyclonal
IsotypeIgG
Host SpeciesRabbit
Tested ApplicationsWB

WB:1:1,000
Species ReactivityHuman
Concentration1mg/ml
Target Information
Alternative NamesA1A antibody A1AT antibody A1AT_HUMAN antibody AAT antibody Alpha 1 antiproteinase antibody Alpha 1 antitrypsin antibody Alpha 1 antitrypsin null antibody Alpha 1 protease inhibitor antibody Alpha-1 protease inhibitor antibody Alpha-1-antiproteinase antibody alpha1 proteinase inhibitor antibody Alpha1AT antibody Dom1 antibody PI antibody PI1 antibody PRO2275 antibody Serine (or cysteine) proteinase inhibitor clade A member 1 antibody Serine protease inhibitor 1-1 antibody Serine protease inhibitor A1a antibody Serpin A1 antibody Serpin A1a antibody Serpin peptidase inhibitor clade A member 1 antibody Serpina1 antibody Short peptide from AAT antibody SPAAT antibody Spi1-1 antibody
Molecular Weight(MW)52 kDa
Cellular LocalizationSecreted
Database Links
SwissProt IDP01009
Application

Application

Fig1: Western blot analysis on human plasma using anti- Alpha 1-Antitrypsin antibody.
Positive ControlHuman plasma
Application NotesWB:1:1,000
Additional Information
FormLiquid
Storage InstructionsStore at +4℃ after thawing. Aliquot store at -20℃ or -80℃. Avoid repeated freeze / thaw cycles.
Storage Buffer1*TBS (pH7.4), 1%BSA, 40%Glycerol. Preservative: 0.05% Sodium Azide.


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